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IEMbase 0377: SCARB1-related scavenger receptor B1 deficiency

Scope

Field Value
IEMbase ID 377
Nosology 15.4.3.01
Gene SCARB1
External IDs OMIM:601040; OMIM:610762
Generated mapping UNMAPPED; low candidate Triple_Negative_Breast_Cancer.yaml#Luminal Androgen Receptor (LAR) TNBC
Candidate DisMech targets No exact local target
Review date 2026-07-07

IEMbase phenotype signal

IEMbase represents SCARB1-related scavenger receptor B1 deficiency, also listed as SRB1 deficiency. Inheritance is listed as autosomal dominant and autosomal recessive.

The cached record is sparse. It lists abnormal platelet function and biochemical rows for serum cholesterol, plasma HDL cholesterol, and serum triglyceride. There are no treatment rows.

DisMech phenotype coverage

There is no exact local DisMech target for SCARB1 deficiency. The generated low candidate Triple_Negative_Breast_Cancer.yaml#Luminal Androgen Receptor (LAR) TNBC is a false positive from weak lexical or biology-adjacent matching. The TNBC file models an oncology subtype defined by absent ER/PR/HER2 expression and tumor pathway biology, not SCARB1-mediated HDL handling or platelet function.

General cardiovascular and lipid-metabolism files may provide downstream context, but no curated SCARB1 deficiency disease entry is present.

Concordance and completeness

Judgement: true local gap; reject the triple-negative breast cancer candidate.

The IEMbase disease is an inherited lipid/HDL receptor disorder involving SCARB1, whereas the generated candidate is a breast cancer molecular subtype. There is no meaningful disease-level concordance.

Curation actions

  • Keep this record unmapped until a SCARB1/SR-BI deficiency target exists.
  • Do not map to Triple_Negative_Breast_Cancer.yaml.
  • If curated, include inheritance heterogeneity, HDL cholesterol, serum cholesterol/triglyceride rows, and abnormal platelet function as review prompts.