Brachydactyly Type A1 phenotype curation notes
Date: 2026-04-19
Scope: phenotype-only curation for kb/disorders/Brachydactyly_Type_A1.yaml
Accepted phenotype assertions
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Type A1 brachydactylyEvidence used: PMID:11455389, PMID:21537345, PMID:32209048 Rationale: multiple abstracts explicitly describe shortening/absence of the middle phalanges, and one multigeneration family reports100% penetrance for phalange phenotype with variable expressivity. -
Short middle phalanx of fingerEvidence used: PMID:34315464, PMID:18629882 Rationale: both abstracts explicitly stateuniform shortening of the middle phalanges in all digits. -
Short middle phalanx of toeEvidence used: PMID:30651074, PMID:40606564 Rationale: both abstracts explicitly include toe involvement (middle bones of fingers and toes;shortening of fingers and/or toes). -
Short statureEvidence used: PMID:34315464 Rationale: direct abstract support in a molecularly confirmed BDA1 family, but stated as variable rather than obligatory.
Claims intentionally not added
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Symphalangism as a standalone phenotype Reason: PMID:40606564 mentions
with or without symphalangism, but the abstract does not specify the joint pattern or body site. More detailed fusion findings in recent reports appear in figure captions/full text and would not survive abstract-only reference validation. -
Specific metacarpal or metatarsal shortening, radial deviation, and digit-by-digit absent phalanges Reason: useful supporting detail exists in figures/full text for PMID:32209048 and PMID:35669189, but not in the cached abstract text.
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Generalized prenatal limb shortening as a disease-level phenotype Reason: PMID:40606564 reports fetal limb shortening, but this currently looks like an isolated prenatal observation rather than a sufficiently established disorder-level phenotype for BDA1.