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Enum: MechanisticNosologyEnum

Classification of diseases by molecular mechanism or affected cellular system. Tag diseases with their primary mechanistic category.

URI: dismech:MechanisticNosologyEnum

Permissible Values

Value Meaning Description
RASopathy MONDO:0021060 RAS/MAPK signaling pathway disorders (Noonan, Costello, CFC, NF1)
ciliopathy MONDO:0005308 Primary cilia structure/function disorders (PKD, Bardet-Biedl, Joubert)
laminopathy MONDO:0021106 Nuclear lamina disorders (EDMD, progeria, lipodystrophy)
collagenopathy MONDO:0004603 Collagen synthesis/structure disorders (OI, EDS, Alport)
mitochondrial disease MONDO:0044970 Mitochondrial function/genome disorders (MELAS, MERRF, Leigh)
tauopathy MONDO:0005574 Tau protein aggregation disorders (Alzheimer's, PSP, CBD)
synucleinopathy MONDO:0000510 Alpha-synuclein aggregation disorders (Parkinson's, DLB, MSA)

Slots

Name Description
classification_value

Identifier and Mapping Information

Schema Source

  • from schema: https://w3id.org/monarch-initiative/dismech

LinkML Source

name: MechanisticNosologyEnum
description: Classification of diseases by molecular mechanism or affected cellular
  system. Tag diseases with their primary mechanistic category.
from_schema: https://w3id.org/monarch-initiative/dismech
rank: 1000
permissible_values:
  RASopathy:
    text: RASopathy
    description: RAS/MAPK signaling pathway disorders (Noonan, Costello, CFC, NF1)
    meaning: MONDO:0021060
  ciliopathy:
    text: ciliopathy
    description: Primary cilia structure/function disorders (PKD, Bardet-Biedl, Joubert)
    meaning: MONDO:0005308
  laminopathy:
    text: laminopathy
    description: Nuclear lamina disorders (EDMD, progeria, lipodystrophy)
    meaning: MONDO:0021106
  collagenopathy:
    text: collagenopathy
    description: Collagen synthesis/structure disorders (OI, EDS, Alport)
    meaning: MONDO:0004603
  mitochondrial disease:
    text: mitochondrial disease
    description: Mitochondrial function/genome disorders (MELAS, MERRF, Leigh)
    meaning: MONDO:0044970
  tauopathy:
    text: tauopathy
    description: Tau protein aggregation disorders (Alzheimer's, PSP, CBD)
    meaning: MONDO:0005574
  synucleinopathy:
    text: synucleinopathy
    description: Alpha-synuclein aggregation disorders (Parkinson's, DLB, MSA)
    meaning: MONDO:0000510