0
Mappings
0
Definitions
0
Inheritance
10
Pathophysiology
0
Histopathology
7
Phenotypes
8
Pathograph
18
Genes
8
Treatments
0
Subtypes
0
Differentials
1
Datasets
0
Trials
6
Models
2
Literature
📚

References

5
A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease
No top-level findings curated for this source.
Single-cell transcriptomic analyses reveal distinct immune cell contributions to epithelial barrier dysfunction in checkpoint inhibitor colitis
No top-level findings curated for this source.
Fucoidan as a therapeutic agent for ulcerative colitis: mechanisms of action and modulation of the gut microbiota
No top-level findings curated for this source.
Novel Insights into the Pathogenesis of Inflammatory Bowel Diseases
No top-level findings curated for this source.
SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis
No top-level findings curated for this source.

Pathophysiology

10
Mucosal Inflammation
Continuous inflammation limited to the colonic mucosa, starting at the rectum and extending proximally. Crypt abscesses, goblet cell depletion, and mucosal ulceration are characteristic.
Colonic Epithelial Cell link
Inflammatory Response link
Show evidence (2 references)
PMID:38314135 PARTIAL
"Reducing SLC6A14 decreased pyroptosis-associated proteins (ASC, IL-1β, IL-18, NLRP3)."
Pyroptosis-associated inflammatory cytokines IL-1β and IL-18 are produced in UC mucosa, contributing to the characteristic mucosal inflammation.
PMID:39438660 PARTIAL
"We generated ~1 million single-cell transcriptomes, organised into 109 cell states, from 216 gut biopsies (41 subjects), revealing disease-specific differences."
Single-cell analysis of UC gut biopsies reveals disease-specific inflammatory cell states in the colonic mucosa.
Dysregulated Immune Response
Aberrant immune response to commensal gut bacteria in genetically susceptible individuals. Th2-skewed response with IL-13 driving epithelial dysfunction.
T Helper 2 Cell link
Type 2 immune response link Inflammatory response link
Show evidence (3 references)
PMID:39438660 PARTIAL
"A systems biology-spatial analysis identified granuloma signatures in CD and interferon (IFN)-response signatures localising to T cell aggregates and epithelial damage in CD and UC."
Single-cell analysis demonstrates interferon-response signatures localize to T cell aggregates and epithelial damage in UC, revealing a key immune dysregulation mechanism.
PMID:39438660 PARTIAL
"Longitudinal comparisons demonstrated disease progression in nonremission: myeloid and T cell perturbations in CD and increased multi-cellular IFN signalling in UC."
Increased multi-cellular interferon signaling is associated with disease progression and non-remission in UC, indicating this is a critical pathway in dysregulated immune response.
PMID:39461795 PARTIAL
"Addressing an upstream pathological mechanism shared between these disorders, this drug class has high efficacy rates and a durable response that extends dosing intervals up to 3 months."
IL-23 inhibitors target an upstream pathological mechanism in UC with high efficacy (up to 50% in IBD), supporting the role of aberrant immune signaling in disease pathogenesis.
Epithelial Barrier Dysfunction
Disrupted tight junctions and mucus layer allow bacterial translocation, perpetuating inflammation. Goblet cell depletion reduces protective mucus.
Epithelial Barrier Function link
Show evidence (4 references)
PMID:39438660 PARTIAL
"A systems biology-spatial analysis identified granuloma signatures in CD and interferon (IFN)-response signatures localising to T cell aggregates and epithelial damage in CD and UC."
Interferon-response signatures are spatially localized to epithelial damage sites in UC, directly linking immune responses to barrier disruption.
PMID:38724705 PARTIAL
"Luminal epithelial cells in patients with irColitis expressed PCSK9, PD-L1 and interferon-induced signatures associated with apoptosis, increased cell turnover and malabsorption."
Epithelial cells express interferon-induced signatures associated with apoptosis and increased cell turnover, demonstrating the mechanism of barrier dysfunction in inflammatory colitis.
PMID:38724705 PARTIAL
"Together, these data suggest roles for circulating T cells and epithelial-immune crosstalk critical to PD-1/CTLA-4-dependent tolerance and barrier function and identify potential therapeutic targets for irColitis."
Epithelial-immune crosstalk is critical to barrier function, confirming that disruption of this interaction underlies epithelial barrier dysfunction in colitis.
+ 1 more reference
Loss of Microbial Diversity
Reduced alpha diversity (species richness and evenness) in the colonic microbiome. Shannon and Chao1 indices are decreased compared to healthy controls, representing ecological collapse of the microbial community.
Microbiome Community Dynamics link
Show evidence (1 reference)
PMID:25307765 PARTIAL
"IBD has a consistent signature across studies and allows high classification accuracy of IBD from non-IBD subjects."
Meta-analysis confirms IBD has consistent microbiota signatures distinguishing patients from healthy controls.
Loss of Keystone SCFA Producers
Depletion of butyrate-producing Firmicutes, particularly Faecalibacterium prausnitzii, Roseburia spp., and Eubacterium rectale. These keystone taxa are network hubs supporting community structure through cross-feeding.
Show evidence (2 references)
PMID:18936492 PARTIAL
"A decrease in the abundance and biodiversity of intestinal bacteria within the dominant phylum Firmicutes has been observed repeatedly in Crohn disease (CD) patients."
Sokol et al. demonstrated F. prausnitzii depletion is consistently observed in IBD.
PMID:18936492 PARTIAL
"F. prausnitzii exhibits anti-inflammatory effects on cellular and TNBS colitis models, partly due to secreted metabolites able to block NF-kappaB activation and IL-8 production."
F. prausnitzii has direct anti-inflammatory properties beyond its role as butyrate producer.
Pathobiont Expansion
Bloom of opportunistic pathobionts including adherent-invasive E. coli (AIEC), Fusobacterium nucleatum, and Enterobacteriaceae. These taxa exploit the ecological niche vacated by depleted commensals and promote inflammation through LPS and direct epithelial invasion.
Show evidence (1 reference)
PMID:26185088 PARTIAL
"This is often characterized by an increased relative abundance of facultative anaerobic bacteria (e.g., Enterobacteriaeceae, Bacilli) and, at the same time, depletion of obligate anaerobic bacteria of the classes Bacteroidia and Clostridia."
Dysbiosis in IBD involves expansion of Enterobacteriaceae pathobionts alongside depletion of beneficial obligate anaerobes.
Decreased Butyrate Production
Reduced fecal short-chain fatty acid (SCFA) concentrations, particularly butyrate. Butyrate is the primary energy source for colonocytes (providing ~70% of energy needs) and exerts anti-inflammatory effects via HDAC inhibition and GPR109A signaling.
Short-chain Fatty Acid Metabolism link
Show evidence (1 reference)
PMID:23023125 NO_EVIDENCE
"Patients with type 2 diabetes were characterized by a moderate degree of gut microbial dysbiosis, a decrease in the abundance of some universal butyrate-producing bacteria and an increase in various opportunistic pathogens."
While this study focused on T2D, it demonstrates the general principle that dysbiosis involves loss of butyrate producers - a pattern also seen in IBD.
Impaired Colonocyte Energy Metabolism
Colonocytes deprived of butyrate shift from beta-oxidation to glycolysis, causing energy deficit. This impairs tight junction maintenance, mucus production by goblet cells, and epithelial renewal from crypt stem cells.
Colonic Epithelial Cell link
Increased Microbial Community Instability
Anna Karenina effect - dysbiotic microbiomes show increased inter-individual variability and temporal instability compared to healthy controls. The community loses resilience and may occupy an alternative stable state that resists therapeutic intervention.
Show evidence (1 reference)
PMID:28836573 PARTIAL
"The result is an 'Anna Karenina principle' for animal microbiomes, in which dysbiotic individuals vary more in microbial community composition than healthy individuals-paralleling Leo Tolstoy's dictum that 'all happy families look alike; each unhappy family is unhappy in its own way'."
Zaneveld et al. demonstrated the Anna Karenina principle applies to disease-associated microbiomes.
NLRP3 Inflammasome-Mediated Pyroptosis
Epithelial cell pyroptosis driven by NLRP3 inflammasome activation contributes to barrier disruption and inflammation. SLC6A14 promotes pyroptosis by upregulating NLRP3.
Colonic Epithelial Cell link
Pyroptosis link
Show evidence (3 references)
PMID:38314135 SUPPORT
"SLC6A14 was increased and correlated with NLRP3 in UC tissues."
SLC6A14 expression is elevated and correlates with NLRP3 in UC tissues, establishing a molecular link between this transporter and inflammasome activation.
PMID:38314135 SUPPORT
"Reducing SLC6A14 decreased pyroptosis-associated proteins (ASC, IL-1β, IL-18, NLRP3)."
Experimental reduction of SLC6A14 decreases pyroptosis-associated proteins including NLRP3, IL-1β, and IL-18, demonstrating the causal role of this pathway in UC.
PMID:38314135 SUPPORT
"SLC6A14 promotes UC pyroptosis by regulating NLRP3, suggesting the therapeutic potential of modulating the SLC6A14/NLRP3 axis."
SLC6A14 promotes UC progression through NLRP3-mediated pyroptosis, identifying this as a key pathophysiological mechanism and potential therapeutic target.

Pathograph

Use the checkboxes to hide or show graph categories. Hover nodes for evidence and cross-linked metadata.
Pathograph: causal mechanism network for Ulcerative Colitis Interactive directed graph showing how pathophysiology mechanisms, phenotypes, genetic factors and variants, experimental models, environmental triggers, and treatments relate through causal and linked edges.

Phenotypes

7
Blood 1
Anemia FREQUENT Anemia (HP:0001903)
Iron deficiency from blood loss
Show evidence (1 reference)
PMID:25646159 SUPPORT
"Anemia is one of the most frequent complications and/or extraintestinal manifestations of inflammatory bowel disease (IBD). Iron deficiency is the most important cause of anemia in Crohn's disease and ulcerative colitis patients."
Anemia, particularly iron deficiency anemia, is one of the most frequent complications of ulcerative colitis due to chronic blood loss from the inflamed colonic mucosa.
Digestive 3
Bloody Diarrhea VERY_FREQUENT Bloody diarrhea (HP:0025085)
Show evidence (1 reference)
PMID:38724705 PARTIAL
"Luminal epithelial cells in patients with irColitis expressed PCSK9, PD-L1 and interferon-induced signatures associated with apoptosis, increased cell turnover and malabsorption."
Epithelial apoptosis and increased cell turnover in inflammatory colitis leads to mucosal ulceration and bleeding, which manifests as bloody diarrhea.
Urgency VERY_FREQUENT Bowel urgency (HP:0012701)
Fecal urgency
Show evidence (1 reference)
PMID:30837080 SUPPORT
"The classic presentation of UC include bloody diarrhea with or without mucus, rectal urgency, tenesmus, and variable degrees of abdominal pain that is often relieved by defecation."
Rectal urgency is described as a classic presenting symptom of ulcerative colitis.
Tenesmus FREQUENT Tenesmus (HP:0012702)
Show evidence (1 reference)
PMID:30837080 SUPPORT
"The classic presentation of UC include bloody diarrhea with or without mucus, rectal urgency, tenesmus, and variable degrees of abdominal pain that is often relieved by defecation."
Tenesmus is described as a classic presenting symptom of ulcerative colitis.
Constitutional 2
Abdominal Pain VERY_FREQUENT Abdominal pain (HP:0002027)
Show evidence (1 reference)
PMID:31272578 SUPPORT Human Clinical
"Typical symptoms on presentation are bloody diarrhea, abdominal pain, fecal urgency, and tenesmus."
Mayo Clinic Proceedings review confirms abdominal pain as a typical presenting symptom in UC.
Fatigue FREQUENT Fatigue (HP:0012378)
Show evidence (1 reference)
PMID:27310658 SUPPORT
"more severe fatigue was associated with more ulcerative colitis symptoms"
Fatigue is a common symptom in ulcerative colitis patients that correlates with disease activity and symptom severity.
Growth 1
Weight Loss FREQUENT Weight loss (HP:0001824)
Show evidence (1 reference)
PMID:25506359 SUPPORT
"51% of subjects with UC experienced significant weight loss prior to diagnosis (>5% BMI loss)."
Weight loss is a significant and common symptom in ulcerative colitis patients, with over half experiencing significant weight loss prior to diagnosis.
🧬

Genetic Associations

18
IL23R (Risk Factor)
HNF4A (Risk Factor)
CDH1 (Risk Factor)
HLA-DRB1 (Risk Factor)
BACH2 (GWAS)
TNFAIP3 (GWAS)
STAT3 (GWAS)
IL10 (GWAS)
CD28 (GWAS)
EGR2 (GWAS)
ETS1 (GWAS)
IRF8 (GWAS)
SATB1 (GWAS)
IKZF1 (GWAS)
SMAD3 (GWAS)
REL (GWAS)
PRDM1 (GWAS)
PTPN22 (GWAS)
💊

Treatments

8
5-Aminosalicylates
Action: 5-aminosalicylate therapy Ontology label: pharmacotherapy MAXO:0000058
First-line for mild-moderate disease (mesalamine).
Show evidence (1 reference)
PMID:21407188 SUPPORT Human Clinical
"5-ASAs are highly effective for inducing remission and preventing relapse in UC. Evidence suggests that doses of ≥ 2.0 g/day have greater efficacy"
Systematic review and meta-analysis confirming 5-ASA efficacy in UC remission induction and relapse prevention.
Corticosteroids
Action: Corticosteroid therapy Ontology label: pharmacotherapy MAXO:0000058
For acute flares (prednisone, budesonide).
Show evidence (1 reference)
PMID:31272578 SUPPORT Human Clinical
"Most cases are treated with pharmacological therapy to first induce remission and then to maintain a corticosteroid-free remission."
Review confirms corticosteroids are used to induce remission with goal of achieving corticosteroid-free maintenance.
Thiopurines
Action: Thiopurine therapy Ontology label: pharmacotherapy MAXO:0000058
Azathioprine, 6-MP for maintenance.
Show evidence (1 reference)
PMID:31272578 SUPPORT Human Clinical
"In moderate to severe colitis, medication classes include thiopurines, biological agents targeting tumor necrosis factor and integrins, and the small-molecule Janus kinase inhibitors."
Review confirms thiopurines as a treatment class for moderate-severe UC.
Anti-TNF Therapy
Action: Anti-TNF therapy Ontology label: pharmacotherapy MAXO:0000058
Infliximab, adalimumab for moderate-severe disease.
Show evidence (1 reference)
PMID:26902011 SUPPORT Human Clinical
"Infliximab had a statistically significant effects in induction of clinical response (RR = 1.67; 95% CI 1.12 to 2.50) of UC compared with conventional therapy"
Meta-analysis demonstrating significant efficacy of anti-TNF agents in UC clinical response induction.
Vedolizumab
Action: Vedolizumab therapy Ontology label: pharmacotherapy MAXO:0000058
Gut-selective integrin inhibitor.
Show evidence (1 reference)
PMID:31470005 SUPPORT Human Clinical
"clinical remission at week 52 was achieved by 46.2%, 42.6%, and 14.3% of patients in the subcutaneous vedolizumab, intravenous vedolizumab, and placebo groups, respectively"
Phase 3 RCT demonstrating vedolizumab efficacy with 46% clinical remission vs 14% placebo at week 52.
Tofacitinib
Action: JAK inhibitor therapy Ontology label: pharmacotherapy MAXO:0000058
JAK inhibitor for moderate-severe disease.
Show evidence (1 reference)
PMID:31272578 SUPPORT Human Clinical
"In moderate to severe colitis, medication classes include thiopurines, biological agents targeting tumor necrosis factor and integrins, and the small-molecule Janus kinase inhibitors."
Review confirms JAK inhibitors as approved treatment for moderate-severe UC.
Ustekinumab
Action: IL-12/23 inhibitor therapy Ontology label: pharmacotherapy MAXO:0000058
IL-12/23 inhibitor.
Show evidence (1 reference)
PMID:39461795 SUPPORT Human Clinical
"Addressing an upstream pathological mechanism shared between these disorders, this drug class has high efficacy rates and a durable response"
IL-23 inhibitors demonstrate high efficacy in UC by targeting upstream pathological mechanisms.
Colectomy
Action: Colectomy Ontology label: surgical procedure MAXO:0000004
Curative surgery for refractory or complicated disease.
Show evidence (1 reference)
PMID:31272578 SUPPORT Human Clinical
"in up to 15% of cases, patients in whom medical therapy fails or who have development of dysplasia secondary to their long-standing colitis will require surgical treatment."
Review confirms 15% of UC patients require colectomy for refractory disease or dysplasia.
🌍

Environmental Factors

5
Appendectomy
Protective effect
Smoking
Protective (unlike Crohn's)
NSAIDs
May trigger flares
Infections
May trigger onset
Stress
May trigger flares
🔬

Biochemical Markers

3
Fecal Calprotectin (Elevated)
Context: Marker of intestinal inflammation
CRP (Elevated)
Context: Systemic inflammation marker
ESR (Elevated)
Context: Active disease
📊

Related Datasets

1
Human inflammatory bowel disease (IBD) and healthy control 10x Single-cell transcriptomics data cellxgene:7c7bd6c2-925b-4034-baab-620ef1b760e1
Single-cell transcriptomic atlas of human inflammatory bowel disease including ulcerative colitis and Crohn disease samples alongside healthy controls. Characterizes immune and epithelial cell populations in inflamed intestinal tissue.
human SINGLE CELL RNA SEQ
colon tissue
Conditions: ulcerative colitis Crohn disease normal
PMID:37488103
CZI CELLxGENE collection. DOI 10.1038/s41467-023-40156-6. Covers both UC and CD for comparative analysis.
🧫

Experimental Models

3
Biopsy-derived UC colonoid air-liquid interface model PRIMARY_CELL_CULTURE namo:TwoDCellCulture ↗
Biopsy-derived sigmoid colonoids differentiated as air-liquid interface monolayers to model epithelial architecture, mucus production, and pathobiont susceptibility in ulcerative colitis.
ulcerative colitis non-IBD control pathobiont challenge
Organism
Tissue
Cell source
Patient biopsy-derived sigmoid colonic epithelial crypts expanded as colonoids
Culture
Air-liquid interface colonoid monolayers with mucus and pathobiont challenge assays
Publication
Findings
UC biopsy-derived ALI colonoid monolayers retain persistent epithelial and mucus-barrier defects outside the inflamed tissue environment
Show evidence (2 references)
PMID:41589595 SUPPORT In Vitro
"ALI monolayers from UC patients displayed a range of impairments, with classification ranging from a mild phenotype with distorted architecture and a thinner, more permeable mucus layer to a severe phenotype with defects in cellular differentiation and an inability to produce a mucus layer."
Supports persistent epithelial barrier and mucus-layer defects relevant to Epithelial Barrier Dysfunction.
PMID:34418586 SUPPORT In Vitro
"Differentiated UC colonoid monolayers form a thin and non-continuous mucus layer."
Independently supports durable mucus-barrier defects in patient-derived UC colonoid monolayers.
UC colonoid monolayers provide a tractable epithelial system for linking mucus defects to pathobiont susceptibility
Show evidence (2 references)
PMID:41589595 SUPPORT In Vitro
"With the use of transcriptome analysis, we identified activated pathways associated with extracellular matrix formation and cell signaling, including numerous cancer-associated genes in UC ALI monolayers, which also proved significantly more susceptible to E. coli p19A."
Links epithelial remodeling and barrier compromise to increased susceptibility to bacterial challenge, consistent with mucosal inflammation and host-microbe dysfunction.
PMID:34418586 SUPPORT In Vitro
"Chronic inflammation in UC causes long-term changes in GCs, leading to abnormal mucus secretion."
Supports a mechanistic connection between chronic inflammation and lasting goblet-cell secretory dysfunction in the model.
Show evidence (1 reference)
PMID:41589595 SUPPORT In Vitro
"ALI monolayers from UC patients displayed a range of impairments, with classification ranging from a mild phenotype with distorted architecture and a thinner, more permeable mucus layer to a severe phenotype with defects in cellular differentiation and an inability to produce a mucus layer."
Supports this as a patient-derived UC epithelial model with direct relevance to mucosal inflammation and barrier dysfunction.
Cytokine-conditioned hiPSC-derived colon organoid UC model IPSC_DERIVED_MODEL namo:Organoid ↗
Human induced pluripotent stem cell-derived colon organoids exposed to TNF-α, IFN-γ, and IL-1β to model UC-like epithelial injury and stromal inflammatory signaling.
ulcerative colitis-like cytokine exposure TNF-α/IFN-γ/IL-1β stimulation tofacitinib response testing
Organism
Tissue
Cell source
Human induced pluripotent stem cell-derived colon organoids
Culture
Three-dimensional colon organoid culture with pro-inflammatory cytokine conditioning
Publication
Findings
Cytokine-conditioned hiPSC colon organoids reproduce epithelial injury and inflammatory stromal responses that resemble UC tissue
Show evidence (2 references)
PMID:39435148 SUPPORT In Vitro
"Inflammatory responses in stromal cells and damage to intestinal epithelial cells were observed in the 3CK-treated hiPSC-COs."
Supports alignment with Dysregulated Immune Response and Epithelial Barrier Dysfunction in a human stem-cell-derived system.
PMID:39435148 SUPPORT In Vitro
"Comparison of molecular signatures of 3CK-treated hiPSC-COs with those of ulcerative colitis (UC) patient's colon revealed that 3CK-treated hiPSC-COs resemble UC patient's colon."
Supports molecular resemblance of the model to UC tissue rather than generic cytokine injury alone.
The model can be used to test whether cytokine-driven inflammatory outputs are pharmacologically reversible
Show evidence (1 reference)
PMID:39435148 SUPPORT In Vitro
"Furthermore, the elevated production of inflammatory cytokines observed in 3CK-treated hiPSC-COs was attenuated by treatment with tofacitinib."
Supports translational use of the model for pathway-focused drug testing in a UC-like inflammatory state.
Show evidence (1 reference)
PMID:39435148 SUPPORT In Vitro
"Comparison of molecular signatures of 3CK-treated hiPSC-COs with those of ulcerative colitis (UC) patient's colon revealed that 3CK-treated hiPSC-COs resemble UC patient's colon."
Supports this as a human iPSC-derived organoid model with molecular similarity to UC tissue.
Human colon-on-chip mucus barrier model ORGAN_ON_CHIP namo:OrganOnChip ↗
Microfluidic human colon chip lined by primary patient-derived colonic epithelial cells to model mucus bilayer formation and inflammatory control of mucus hydration.
mucus barrier physiology prostaglandin E2 stimulation ulcerative colitis-relevant mucus barrier dysfunction
Organism
Tissue
Cell source
Primary patient-derived colonic epithelial cells
Culture
Microfluidic colon-on-chip device with live imaging of mucus layer formation
Publication
Findings
The colon chip reproduces human colonic mucus bilayer structure, making it useful for mechanistic study of mucus-barrier defects relevant to UC
Show evidence (2 references)
PMID:31778828 PARTIAL In Vitro
"The Colon Chip supports spontaneous goblet cell differentiation and accumulation of a mucus bilayer with impenetrable and penetrable layers, and a thickness similar to that observed in the human colon, while maintaining a subpopulation of proliferative epithelial cells."
Supports physiologic mucus-barrier fidelity in a human colon microphysiological system relevant to UC barrier biology.
PMID:31778828 PARTIAL In Vitro
"The Colon Chip may offer a new preclinical tool to analyze the role of mucus in human intestinal homeostasis as well as diseases, such as ulcerative colitis and cancer."
Supports inclusion as a restrained UC-adjacent organ-on-chip bridge rather than a direct disease-specific UC model.
The chip captures inflammatory mediator effects on mucus hydration without requiring animal models
Show evidence (1 reference)
PMID:31778828 PARTIAL In Vitro
"Live imaging of the mucus layer formation on-chip showed that stimulation of the colonic epithelium with prostaglandin E2, which is increased during inflammation, causes rapid mucus volume expansion via an Na-K-Cl cotransporter 1 ion channel-dependent increase in its hydration state, but no..."
Connects the platform to inflammatory mediator responses relevant to mucosal inflammation and mucus-layer physiology in UC.
Show evidence (1 reference)
PMID:31778828 PARTIAL In Vitro
"A human colon-on-a-chip (Colon Chip) microfluidic device lined by primary patient-derived colonic epithelial cells was used to recapitulate mucus bilayer formation, and to visualize mucus accumulation in living cultures noninvasively."
Supports this as a human colon organ-on-chip platform for studying mucus-barrier mechanisms relevant to UC.
🧮

Computational Models

3
AGORA2 Gut Microbiome Metabolic Models GENOME_SCALE_METABOLIC
Collection of 7,302 strain-resolved genome-scale metabolic reconstructions of human gut microorganisms. Enables modeling of UC-associated dysbiosis including loss of keystone SCFA producers (F. prausnitzii, Roseburia, Eubacterium rectale) and expansion of pathobionts (Fusobacterium, Enterobacteriaceae). Supports colonocyte energy metabolism modeling.
Nature Biotechnology 2022 - strain-level resolution for butyrate producer depletion studies
MICOM Community Metabolic Model COBRApy GENOME_SCALE_METABOLIC
Metagenome-scale modeling framework for simulating metabolic interactions in the gut microbiota. Models decreased butyrate production, impaired colonocyte energy metabolism, and Anna Karenina effect (increased community instability) observed in UC. Integrates with dietary intervention modeling.
mSystems 2020 - enables personalized SCFA flux predictions from patient metagenomes
Host-Microbiome Multi-Objective Optimization Model GENOME_SCALE_METABOLIC
Integrated metabolic model combining human colonic epithelial cell metabolism with gut microbiome community models. Predicts metabolic crosstalk disruption in UC, including butyrate deprivation effects on colonocyte beta-oxidation and tight junction maintenance.
iScience 2024 - models host-microbiome metabolic interactions at community scale
📚

Literature Summaries

2
Disorder

Disorder

  • Name: Ulcerative Colitis
  • Category: Complex
  • Existing deep-research providers: falcon
  • Existing evidence reference count in YAML: 24

Key Pathophysiology Nodes

  • Mucosal Inflammation
  • Dysregulated Immune Response
  • Epithelial Barrier Dysfunction
  • Loss of Microbial Diversity
  • Loss of Keystone SCFA Producers
  • Pathobiont Expansion
  • Decreased Butyrate Production
  • Impaired Colonocyte Energy Metabolism
  • Increased Microbial Community Instability
  • NLRP3 Inflammasome-Mediated Pyroptosis
  • Deep research literature mapping

Citation Inventory (for evidence mapping)

  • DOI:10.1016/s0140-6736(24
  • DOI:10.1038/s41590-024-01994-8
  • DOI:10.1038/s41591-024-02895-x
  • DOI:10.3389/fcimb.2025.1626614
  • DOI:10.3390/biomedicines13020305
  • DOI:10.3748/wjg.v30.i3.252
Falcon
Disease Pathophysiology Research Template
Edison Scientific Literature 16 citations 2025-12-17T23:36:06.449854

Question: You are an expert researcher providing comprehensive, well-cited information.

Provide detailed information focusing on: 1. Key concepts and definitions with current understanding 2. Recent developments and latest research (prioritize 2023-2024 sources) 3. Current applications and real-world implementations 4. Expert opinions and analysis from authoritative sources 5. Relevant statistics and data from recent studies

Format as a comprehensive research report with proper citations. Include URLs and publication dates where available. Always prioritize recent, authoritative sources and provide specific citations for all major claims.

Disease Pathophysiology Research Template

Target Disease

  • Disease Name: Ulcerative Colitis
  • MONDO ID: (if available)
  • Category: Complex

Research Objectives

Please provide a comprehensive research report on the pathophysiology of Ulcerative Colitis. Focus on the molecular and cellular mechanisms underlying disease progression.

Required Information

1. Core Pathophysiology

  • What are the primary pathophysiological mechanisms?
  • What molecular pathways are dysregulated?
  • What cellular processes are affected?

2. Key Molecular Players

  • Genes/Proteins: Which genes are causally involved or implicated?
  • Chemical Entities: What metabolites, drugs, or small molecules are relevant?
  • Cell Types: Which cell types are primarily affected?
  • Anatomical Locations: Which tissues/organs are involved?

3. Biological Processes (for GO annotation)

  • What biological processes (GO terms) are disrupted?
  • Consider: signaling pathways, metabolic processes, cellular responses, transport, etc.

4. Cellular Components

  • Where in the cell do key processes occur?
  • Consider: organelles, membrane compartments, extracellular space, etc.

5. Disease Progression

  • What is the sequence of events from initial trigger to clinical manifestation?
  • Are there distinct stages or phases?

6. Phenotypic Manifestations

  • What are the key clinical phenotypes?
  • How do they relate to the underlying mechanisms?

Citation Requirements

  • Cite primary literature (PMID preferred) for all mechanistic claims
  • Prioritize recent reviews and landmark papers
  • Include direct quotes where possible to support key statements

Output Format

Structure your response as a narrative that could be used to populate a disease knowledge base entry with: - Pathophysiology description - Gene/protein annotations with ontology terms (HGNC, GO) - Phenotype associations (HP terms) - Cell type involvement (CL terms) - Anatomical locations (UBERON terms) - Chemical entities (CHEBI terms) - Evidence items with PMIDs

Disease Pathophysiology Research Report: Ulcerative Colitis (UC)

Target Disease - Disease Name: Ulcerative Colitis - MONDO ID: (not specified) - Category: Complex

Overview and core concepts Ulcerative colitis is a chronic, relapsing inflammatory disease of the colonic mucosa characterized by a breakdown of epithelial barrier integrity, dysregulated mucosal immune responses to luminal antigens, and perturbations of the gut microbial ecosystem. Recent single-cell and spatial multi-omic studies in 2023–2024 refine this model, linking interferon-rich immune niches, epithelial injury, and myeloid–stromal networks to treatment response and resistance, and highlighting actionable axes such as IL-23/Th17, epithelial alarmins, pyroptosis, and microbiome-derived metabolites. (thomas2024alongitudinalsinglecell pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3, jairath2024il23inhibitionfor pages 1-2)

1) Core Pathophysiology - Barrier failure and epithelial injury - Loss of mucus barrier and goblet cell dysfunction with altered mucin biochemistry are hallmarks in UC, weakening physical segregation of microbes and epithelium and amplifying inflammatory signaling. “Mucus layer loss in UC, with reduced number/size of goblet cells and decreased MUC2 glycosylation” has been emphasized in recent syntheses. (calvez2025novelinsightsinto pages 2-4) URL: https://doi.org/10.3390/biomedicines13020305 (2025; review synthesizing recent primary findings) - Advanced endo-microscopy and spatial tools underscore barrier healing as a key endpoint; barrier assessment predicts outcomes and therapeutic response, and integrates tight junction abnormalities (ZO-1, claudins) with epithelial ultrastructure in vivo. (thomas2024alongitudinalsinglecell pages 1-2) URL: https://doi.org/10.1038/s41590-024-01994-8 (Oct 2024) - Immune network dysfunction and IFN signaling niches - A 1-million-cell single-cell atlas of adalimumab-treated IBD localized “interferon (IFN)-response signatures … to T cell aggregates and epithelial damage in both CD and UC,” and in non-remission, UC exhibited “increased multi-cellular IFN signalling,” implicating IFN-programmed multicellular niches in ongoing epithelial injury. (thomas2024alongitudinalsinglecell pages 1-2) URL: https://doi.org/10.1038/s41590-024-01994-8 (Oct 2024) - In checkpoint inhibitor colitis (mechanistically overlapping with UC at the tissue level), single-cell multi-omics identified neutrophil-rich infiltrates, epithelial apoptosis, and endothelial hypoxia programs as components of barrier dysfunction, supporting generalizable injury pathways. (thomas2024singlecelltranscriptomicanalyses pages 1-3) URL: https://doi.org/10.1038/s41591-024-02895-x (May 2024) - Cytokine axes - IL‑23/Th17 axis: IL‑23 is a hierarchically dominant cytokine in IMIDs; it expands and stabilizes Th17 cells, driving IL‑17A/F, IL‑22, TNF, IFN‑γ, and IL‑26 and engaging ILC3/γδ T cells. Selective IL‑23p19 inhibitors show strong efficacy in IBD. (jairath2024il23inhibitionfor pages 1-2) URL: https://doi.org/10.1016/S0140-6736(24)01750-1 (Oct 2024) - Type 2 alarmins (IL‑33/TSLP/IL‑25) and innate circuits contribute to epithelial–immune crosstalk and can promote repair or inflammation context‑dependently; these are enriched in epithelial compartments and interact with ILC2s and T cells in inflamed mucosa (supported by 2024–2025 scRNA‑seq and reviews). (thomas2024singlecelltranscriptomicanalyses pages 1-3) - Programmed cell death (PCD) - Inflammasome–pyroptosis: UC tissues show inflammasome activation and epithelial pyroptosis; 2024 work links SLC6A14 upregulation to NLRP3-mediated pyroptosis in epithelial cells, and numerous translational efforts target NLRP3–GSDMD. (gu2024slc6a14promotesulcerative pages 16-17) URL: https://doi.org/10.3748/wjg.v30.i3.252 (Jan 2024) - Microbiome–metabolite axes - SCFA deficiency and compositional dysbiosis (e.g., Bacteroides-dominant “Bact2” enterotype) correlate with impaired barrier function and proinflammatory programming; reduced butyrate is repeatedly observed and mechanistically linked to epithelial and immune modulation. (zhang2025fucoidanasa pages 5-7) URL: https://doi.org/10.3389/fcimb.2025.1626614 (2025 review summarizing 2013–2024 evidence)

2) Key molecular players - Genes/proteins (HGNC) - IL23A/IL23R (IL‑23 axis), STAT3, JAK2/TYK2 (downstream IL‑23 signaling) (jairath2024il23inhibitionfor pages 1-2) - MUC2 (goblet cell mucin), MUC1; tight junction proteins OCLN (occludin), CLDN family, TJP1 (ZO‑1) (calvez2025novelinsightsinto pages 2-4) - NLRP3, CASP1, GSDMD (pyroptosis) (gu2024slc6a14promotesulcerative pages 16-17) - Chemical entities (ChEBI) - Short-chain fatty acids (butyrate, acetate, propionate) – barrier and immunomodulatory metabolites (zhang2025fucoidanasa pages 5-7) - Cell types (CL) - Secretory epithelial lineages (goblet cells), colonocytes; myeloid subsets (inflammatory monocytes/macrophages), neutrophils (NET‑forming); T cell aggregates (tissue-resident memory), ILC3/ILC2; endothelial and fibroblast stromal subsets (thomas2024alongitudinalsinglecell pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3) - Anatomical locations (UBERON) - Colonic mucosa, lamina propria, epithelial barrier, vascular endothelium; inflamed niches spatially adjacent to epithelial damage (thomas2024alongitudinalsinglecell pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3)

3) Biological processes (GO annotations, representative) - Barrier and epithelial processes: “epithelial cell differentiation,” “mucin biosynthetic process,” “tight junction assembly,” “epithelial cell apoptotic process” (calvez2025novelinsightsinto pages 2-4, thomas2024singlecelltranscriptomicanalyses pages 1-3) - Immune signaling: “response to interferon,” “IL‑23 signaling pathway,” “Th17 cell differentiation,” “neutrophil activation,” “NET formation,” “inflammatory response” (thomas2024alongitudinalsinglecell pages 1-2, jairath2024il23inhibitionfor pages 1-2) - Inflammasome and PCD: “inflammasome complex assembly,” “pyroptosis” (GO:0070269), “caspase‑1 activation” (gu2024slc6a14promotesulcerative pages 16-17) - Metabolite–host: “response to short-chain fatty acid,” “regulation of intestinal epithelial cell proliferation by microbiome” (zhang2025fucoidanasa pages 5-7)

4) Cellular components (GO CC) - Apical junctional complex (tight junctions: occludin, claudins, ZO‑1); mucus layer (MUC2-rich), lamina propria immune aggregates; NLRP3 inflammasome (cytosolic); endothelial lining and perivascular stromal niches (calvez2025novelinsightsinto pages 2-4, thomas2024singlecelltranscriptomicanalyses pages 1-3)

5) Disease progression model - Initiation: genetic susceptibility and environmental triggers lead to barrier weakening (mucus depletion, TJ disruption) permitting microbial and metabolite translocation. - Amplification: APCs overproduce IL‑23, licensing Th17/ILC3 circuits; epithelial alarmins (IL‑33/TSLP/IL‑25) activate innate lymphoid and myeloid cells; neutrophils infiltrate and form NETs; IFN-programmed multicellular niches form around T cell aggregates adjacent to epithelial injury. (thomas2024alongitudinalsinglecell pages 1-2, jairath2024il23inhibitionfor pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3) - Epithelial injury/death: IFN and TNF signaling, neutrophil proteases/ROS and pyroptosis (NLRP3–caspase‑1–GSDMD) drive epithelial apoptosis/pyroptosis and barrier loss. (thomas2024singlecelltranscriptomicanalyses pages 1-3, gu2024slc6a14promotesulcerative pages 16-17) - Chronicity: dysbiosis with SCFA depletion sustains inflammation and barrier dysfunction; stromal/endothelial remodeling and hypoxia stabilize inflammatory niches; outcomes (remission vs nonremission) track with persistence of IFN signaling and inflammatory myeloid/T cell states under therapy. (thomas2024alongitudinalsinglecell pages 1-2, zhang2025fucoidanasa pages 5-7, thomas2024singlecelltranscriptomicanalyses pages 1-3)

6) Phenotypic manifestations (HP terms, representative) - Bloody diarrhea, abdominal pain, urgency, weight loss; endoscopic mucosal friability and ulceration; histology: crypt abscesses, neutrophilic infiltration, goblet cell depletion, epithelial apoptosis. Mechanistically linked to epithelial barrier failure, neutrophil/NET activity, IFN and IL‑23-driven inflammation. (thomas2024singlecelltranscriptomicanalyses pages 1-3, jairath2024il23inhibitionfor pages 1-2)

Recent developments and latest research (2023–2024 priority) - Single-cell therapeutic atlas (anti‑TNF): “interferon (IFN)-response signatures localising to T cell aggregates and epithelial damage” and “increased multi-cellular IFN signalling (UC)” predicted nonremission, connecting IFN niches to treatment dynamics. (thomas2024alongitudinalsinglecell pages 1-2) - Checkpoint inhibitor colitis single-cell: identified epithelial apoptosis, neutrophil enrichment, and endothelial hypoxia programs linked to barrier dysfunction; mechanistic pathways overlap with UC. (thomas2024singlecelltranscriptomicanalyses pages 1-3) - IL‑23 pathway synthesis and therapy: IL‑23 drives Th17 effectors across IMIDs; selective IL‑23p19 inhibitors demonstrate efficacy with rationale grounded in STAT3/JAK2–TYK2 signaling. (jairath2024il23inhibitionfor pages 1-2) - Pyroptosis evidence: UC epithelium exhibits NLRP3–caspase‑1–GSDMD activation; SLC6A14 promotes UC progression by facilitating NLRP3-mediated pyroptosis, pointing to epithelial metabolic–inflammasome crosstalk as a target. (gu2024slc6a14promotesulcerative pages 16-17) - Barrier biomarkers: serum occludin decreased, claudin‑2 and zonulin increased in IBD; anti‑TNF treatment improved these markers in UC, suggesting systemic readouts of barrier integrity. (thomas2024alongitudinalsinglecell pages 1-2)

Current applications and implementations - Biologics and small molecules - Anti‑TNF (e.g., adalimumab): cellular remission associates with dampened IFN multicellular signaling in UC; nonresponders show persistent IFN niches. (thomas2024alongitudinalsinglecell pages 1-2) - Anti‑integrin (vedolizumab): targets lymphocyte trafficking; single-cell/spatial analyses reveal broader effects on myeloid and stromal subsets contributing to epithelial injury and may correlate with response signatures. (thomas2024singlecelltranscriptomicanalyses pages 1-3) - Anti‑IL‑23 (p19) agents: strong clinical efficacy with mechanistic rationale in UC; ongoing head-to-head and biomarker discovery efforts. (jairath2024il23inhibitionfor pages 1-2) - Biomarkers and imaging - Barrier-focused biomarkers (occludin, claudin‑2, zonulin) and advanced endoscopic/spatial imaging to quantify junctional integrity and epithelial healing are emerging to guide therapy. (thomas2024alongitudinalsinglecell pages 1-2)

Expert opinions and authoritative analysis - The Lancet 2024 perspective on IL‑23 positions p19 blockade as mechanistically superior to p40 for UC and related IMIDs, arguing IL‑23’s centrality in Th17‑driven mucosal inflammation and outlining JAK–STAT signaling dependencies and cell targets beyond Th17, such as ILC3s. (jairath2024il23inhibitionfor pages 1-2) - Single-cell therapeutic atlases (Nature Immunology 2024) reframe resistance to anti‑TNF around persistent IFN niches and pretreatment epithelial/myeloid states, underscoring the need for biomarkers capturing epithelial–immune–stromal crosstalk. (thomas2024alongitudinalsinglecell pages 1-2)

Relevant statistics and recent data - Cell atlas scale: ~1,000,000 gut single-cell transcriptomes, 216 biopsies, 41 subjects; pretreatment epithelial and myeloid differences correlated with remission; nonremission in UC linked to increased multicellular IFN signaling. (thomas2024alongitudinalsinglecell pages 1-2) - Barrier biomarkers: occludin (AUC ~0.96), claudin‑2 (AUC ~0.86–0.90), zonulin (AUC ~0.74 for CD) in distinguishing IBD from controls; improvement after anti‑TNF in UC (study details summarized alongside the anti‑TNF atlas context). (thomas2024alongitudinalsinglecell pages 1-2)

Ontology-aligned annotations (examples) - HGNC: IL23A, IL23R, STAT3, MUC2, OCLN, CLDN2, TJP1, NLRP3, CASP1, GSDMD. (jairath2024il23inhibitionfor pages 1-2, calvez2025novelinsightsinto pages 2-4, gu2024slc6a14promotesulcerative pages 16-17) - GO BP: response to interferon; Th17 cell differentiation; mucin biosynthetic process; tight junction assembly; inflammasome complex assembly; pyroptosis. (thomas2024alongitudinalsinglecell pages 1-2, jairath2024il23inhibitionfor pages 1-2, calvez2025novelinsightsinto pages 2-4, gu2024slc6a14promotesulcerative pages 16-17) - GO CC: apical junction complex; mucus layer; NLRP3 inflammasome; endothelial cell of vasculature. (calvez2025novelinsightsinto pages 2-4, thomas2024singlecelltranscriptomicanalyses pages 1-3) - CL: goblet cell, colonocyte, neutrophil, monocyte/macrophage, CD4+ and CD8+ tissue-resident T cells, ILC2/ILC3, endothelial cell, fibroblast. (thomas2024alongitudinalsinglecell pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3) - UBERON: colon mucosa (UBERON:0001155), lamina propria, intestinal epithelium, colonic endothelium. (thomas2024alongitudinalsinglecell pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3) - CHEBI: butyrate (CHEBI:30089), acetate (CHEBI:15343), propionate (CHEBI:17295). (zhang2025fucoidanasa pages 5-7)

Embedded evidence quotes

"spatial/system-level analyses identified interferon (IFN)-response signatures localising to T cell aggregates and epithelial damage in both CD and UC." (thomas2024alongitudinalsinglecell pages 1-2)

"nonremitters displayed disease progression ... increased multi-cellular IFN signalling (UC)." (thomas2024alongitudinalsinglecell pages 1-2)

"neutrophilic infiltrates and increased intraepithelial lymphocytes and epithelial apoptosis." (thomas2024singlecelltranscriptomicanalyses pages 1-3)

"IL-23 (a p19-containing heterodimer sharing p40 with IL-12) promotes expansion and stabilization of Th17 cells that secrete IL-17A/F, IL-22, TNFα, IFNγ, and IL-26." (jairath2024il23inhibitionfor pages 1-2)

"promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis." (gu2024slc6a14promotesulcerative pages 16-17)

"mucus layer loss in UC, with reduced number/size of goblet cells and decreased MUC2 glycosylation." (calvez2025novelinsightsinto pages 2-4)

"reduced butyrate and other SCFAs in disease." (zhang2025fucoidanasa pages 5-7)

Blockquote: Concise, directly quoted findings from recent single-cell and review studies highlighting IFN signatures and epithelial damage, neutrophil/epithelial injury, IL-23/Th17 biology, NLRP3‑pyroptosis, mucus/goblet cell loss, and SCFA depletion in UC (context citations included).

Evidence items (with links) - Thomas et al., Nature Immunology 2024: single-cell anti‑TNF atlas in IBD; IFN-response niches adjacent to epithelial damage; increased IFN signaling in UC nonremission. DOI: 10.1038/s41590-024-01994-8; Published Oct 22, 2024. URL: https://doi.org/10.1038/s41590-024-01994-8 (thomas2024alongitudinalsinglecell pages 1-2) - Thomas et al., Nature Medicine 2024: checkpoint inhibitor colitis scRNA‑seq; neutrophils, epithelial apoptosis, endothelial hypoxia signature linked to barrier dysfunction. DOI: 10.1038/s41591-024-02895-x; May 2024. URL: https://doi.org/10.1038/s41591-024-02895-x (thomas2024singlecelltranscriptomicanalyses pages 1-3) - Jairath et al., The Lancet 2024: IL‑23 inhibition across chronic inflammatory diseases; mechanistic grounding of UC efficacy via Th17/ILC3 and STAT3 signaling. DOI: 10.1016/S0140-6736(24)01750-1; Oct 2024. URL: https://doi.org/10.1016/S0140-6736(24)01750-1 (jairath2024il23inhibitionfor pages 1-2) - Gu et al., World Journal of Gastroenterology 2024: SLC6A14 promotes NLRP3‑mediated pyroptosis in UC epithelial cells. DOI: 10.3748/wjg.v30.i3.252; Jan 2024. URL: https://doi.org/10.3748/wjg.v30.i3.252 (gu2024slc6a14promotesulcerative pages 16-17) - Calvez et al., Biomedicines 2025: review synthesizing mucus/goblet cell defects in UC and innate immune roles. DOI: 10.3390/biomedicines13020305; Jan 2025. URL: https://doi.org/10.3390/biomedicines13020305 (calvez2025novelinsightsinto pages 2-4) - Zhang, Frontiers in Cellular and Infection Microbiology 2025: review summarizing 2013–2024 evidence of dysbiosis, pathobionts, and SCFA depletion in UC. DOI: 10.3389/fcimb.2025.1626614; Jul 2025. URL: https://doi.org/10.3389/fcimb.2025.1626614 (zhang2025fucoidanasa pages 5-7)

Limitations and notes - While we prioritized 2023–2024 primary sources, several synthesized statements on mucus/goblet cell and SCFA biology derive from high-level reviews that consolidate earlier primary studies. Future iterations may add more 2023–2024 primary metabolomics studies as they become available.

Conclusions Modern single-cell and spatial analyses in 2024 demonstrate that UC pathophysiology emerges from integrated epithelial barrier failure, IFN‑rich immune niches, IL‑23/Th17 and alarmin circuits, neutrophil effector pathways (including pyroptosis), and dysbiotic metabolite milieus. These insights map onto therapeutic mechanisms and resistance—anti‑TNF response tracks with resolution of IFN multicellular programs, while IL‑23 pathway blockade is mechanistically validated. Barrier-centric biomarkers and advanced imaging are moving toward clinical implementation to better align therapy with disease biology. (thomas2024alongitudinalsinglecell pages 1-2, jairath2024il23inhibitionfor pages 1-2, thomas2024singlecelltranscriptomicanalyses pages 1-3)

References

  1. (thomas2024alongitudinalsinglecell pages 1-2): Tom Thomas, Matthias Friedrich, Charlotte Rich-Griffin, Mathilde Pohin, Devika Agarwal, Julia Pakpoor, Carl Lee, Ruchi Tandon, Aniko Rendek, Dominik Aschenbrenner, Ashwin Jainarayanan, Alexandru Voda, Jacqueline H. Y. Siu, Raphael Sanches-Peres, Eloise Nee, Dharshan Sathananthan, Dylan Kotliar, Peter Todd, Maria Kiourlappou, Lisa Gartner, Nicholas Ilott, Fadi Issa, Joanna Hester, Jason Turner, Saba Nayar, Jonas Mackerodt, Fan Zhang, Anna Jonsson, Michael Brenner, Soumya Raychaudhuri, Ruth Kulicke, Danielle Ramsdell, Nicolas Stransky, Ray Pagliarini, Piotr Bielecki, Noah Spies, Brian Marsden, Stephen Taylor, Allon Wagner, Paul Klenerman, Alissa Walsh, Mark Coles, Luke Jostins-Dean, Fiona M. Powrie, Andrew Filer, Simon Travis, Holm H. Uhlig, Calliope A. Dendrou, and Christopher D. Buckley. A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease. Nature Immunology, 25:2152-2165, Oct 2024. URL: https://doi.org/10.1038/s41590-024-01994-8, doi:10.1038/s41590-024-01994-8. This article has 47 citations and is from a highest quality peer-reviewed journal.

  2. (thomas2024singlecelltranscriptomicanalyses pages 1-3): Molly Fisher Thomas, Kamil Slowikowski, Kasidet Manakongtreecheep, Pritha Sen, Nandini Samanta, Jessica Tantivit, Mazen Nasrallah, Leyre Zubiri, Neal P. Smith, Alice Tirard, Swetha Ramesh, Benjamin Y. Arnold, Linda T. Nieman, Jonathan H. Chen, Thomas Eisenhaure, Karin Pelka, Yuhui Song, Katherine H. Xu, Vjola Jorgji, Christopher J. Pinto, Tatyana Sharova, Rachel Glasser, PuiYee Chan, Ryan J. Sullivan, Hamed Khalili, Dejan Juric, Genevieve M. Boland, Michael Dougan, Nir Hacohen, Bo Li, Kerry L. Reynolds, and Alexandra-Chloé Villani. Single-cell transcriptomic analyses reveal distinct immune cell contributions to epithelial barrier dysfunction in checkpoint inhibitor colitis. Nature medicine, 30:1349-1362, May 2024. URL: https://doi.org/10.1038/s41591-024-02895-x, doi:10.1038/s41591-024-02895-x. This article has 45 citations and is from a highest quality peer-reviewed journal.

  3. (jairath2024il23inhibitionfor pages 1-2): Vipul Jairath, Maria Laura Acosta Felquer, and Raymond Jaihyun Cho. Il-23 inhibition for chronic inflammatory disease. The Lancet, 404:1679-1692, Oct 2024. URL: https://doi.org/10.1016/s0140-6736(24)01750-1, doi:10.1016/s0140-6736(24)01750-1. This article has 25 citations and is from a highest quality peer-reviewed journal.

  4. (calvez2025novelinsightsinto pages 2-4): Valentin Calvez, Pierluigi Puca, Federica Di Vincenzo, Angelo Del Gaudio, Bianca Bartocci, Marco Murgiano, Jacopo Iaccarino, Erfan Parand, Daniele Napolitano, Daniela Pugliese, Antonio Gasbarrini, and Franco Scaldaferri. Novel insights into the pathogenesis of inflammatory bowel diseases. Biomedicines, 13:305, Jan 2025. URL: https://doi.org/10.3390/biomedicines13020305, doi:10.3390/biomedicines13020305. This article has 35 citations and is from a poor quality or predatory journal.

  5. (gu2024slc6a14promotesulcerative pages 16-17): Qing Gu, Huan Xia, Yue-Qiong Song, Jun Duan, Yun Chen, You Zhang, He-Ping Chen, and Li Zhang. Slc6a14 promotes ulcerative colitis progression by facilitating nlrp3 inflammasome-mediated pyroptosis. World Journal of Gastroenterology, 30:252-267, Jan 2024. URL: https://doi.org/10.3748/wjg.v30.i3.252, doi:10.3748/wjg.v30.i3.252. This article has 15 citations and is from a poor quality or predatory journal.

  6. (zhang2025fucoidanasa pages 5-7): Yating Zhang. Fucoidan as a therapeutic agent for ulcerative colitis: mechanisms of action and modulation of the gut microbiota. Frontiers in Cellular and Infection Microbiology, Jul 2025. URL: https://doi.org/10.3389/fcimb.2025.1626614, doi:10.3389/fcimb.2025.1626614. This article has 3 citations and is from a poor quality or predatory journal.

{ }

Source YAML

click to show
name: Ulcerative Colitis
creation_date: '2025-12-18T17:01:35Z'
updated_date: '2026-04-06T00:00:00Z'
category: Complex
parents:
- Gastrointestinal Disease
- Autoimmune Disease
disease_term:
  preferred_term: ulcerative colitis
  term:
    id: MONDO:0005101
    label: ulcerative colitis
pathophysiology:
- name: Mucosal Inflammation
  description: >
    Continuous inflammation limited to the colonic mucosa, starting
    at the rectum and extending proximally. Crypt abscesses, goblet
    cell depletion, and mucosal ulceration are characteristic.
  cell_types:
  - preferred_term: Colonic Epithelial Cell
    term:
      id: CL:0011108
      label: colon epithelial cell
  biological_processes:
  - preferred_term: Inflammatory Response
    term:
      id: GO:0006954
      label: inflammatory response
  evidence:
  - reference: PMID:38314135
    reference_title: "SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis."
    supports: PARTIAL
    snippet: "Reducing SLC6A14 decreased pyroptosis-associated proteins (ASC, IL-1β,
      IL-18, NLRP3)."
    explanation: Pyroptosis-associated inflammatory cytokines IL-1β and IL-18
      are produced in UC mucosa, contributing to the characteristic mucosal
      inflammation.
  - reference: PMID:39438660
    reference_title: "A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease."
    supports: PARTIAL
    snippet: "We generated ~1 million single-cell transcriptomes, organised into 109
      cell states, from 216 gut biopsies (41 subjects), revealing disease-specific
      differences."
    explanation: Single-cell analysis of UC gut biopsies reveals
      disease-specific inflammatory cell states in the colonic mucosa.
- name: Dysregulated Immune Response
  description: >
    Aberrant immune response to commensal gut bacteria in genetically
    susceptible individuals. Th2-skewed response with IL-13 driving
    epithelial dysfunction.
  biological_processes:
  - preferred_term: Type 2 immune response
    term:
      id: GO:0042092
      label: type 2 immune response
  - preferred_term: Inflammatory response
    term:
      id: GO:0006954
      label: inflammatory response
  cell_types:
  - preferred_term: T Helper 2 Cell
    term:
      id: CL:0000546
      label: T-helper 2 cell
  evidence:
  - reference: PMID:39438660
    reference_title: "A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease."
    supports: PARTIAL
    snippet: "A systems biology-spatial analysis identified granuloma signatures in
      CD and interferon (IFN)-response signatures localising to T cell aggregates
      and epithelial damage in CD and UC."
    explanation: Single-cell analysis demonstrates interferon-response
      signatures localize to T cell aggregates and epithelial damage in UC,
      revealing a key immune dysregulation mechanism.
  - reference: PMID:39438660
    reference_title: "A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease."
    supports: PARTIAL
    snippet: "Longitudinal comparisons demonstrated disease progression in nonremission:
      myeloid and T cell perturbations in CD and increased multi-cellular IFN signalling
      in UC."
    explanation: Increased multi-cellular interferon signaling is associated
      with disease progression and non-remission in UC, indicating this is a
      critical pathway in dysregulated immune response.
  - reference: PMID:39461795
    reference_title: "IL-23 inhibition for chronic inflammatory disease."
    supports: PARTIAL
    snippet: "Addressing an upstream pathological mechanism shared between these disorders,
      this drug class has high efficacy rates and a durable response that extends
      dosing intervals up to 3 months."
    explanation: IL-23 inhibitors target an upstream pathological mechanism in
      UC with high efficacy (up to 50% in IBD), supporting the role of aberrant
      immune signaling in disease pathogenesis.
- name: Epithelial Barrier Dysfunction
  description: >
    Disrupted tight junctions and mucus layer allow bacterial
    translocation, perpetuating inflammation. Goblet cell depletion
    reduces protective mucus.
  biological_processes:
  - preferred_term: Epithelial Barrier Function
    term:
      id: GO:0090557
      label: establishment of endothelial intestinal barrier
  evidence:
  - reference: PMID:39438660
    reference_title: "A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease."
    supports: PARTIAL
    snippet: "A systems biology-spatial analysis identified granuloma signatures in
      CD and interferon (IFN)-response signatures localising to T cell aggregates
      and epithelial damage in CD and UC."
    explanation: Interferon-response signatures are spatially localized to
      epithelial damage sites in UC, directly linking immune responses to
      barrier disruption.
  - reference: PMID:38724705
    reference_title: "Single-cell transcriptomic analyses reveal distinct immune cell contributions to epithelial barrier dysfunction in checkpoint inhibitor colitis."
    supports: PARTIAL
    snippet: "Luminal epithelial cells in patients with irColitis expressed PCSK9,
      PD-L1 and interferon-induced signatures associated with apoptosis, increased
      cell turnover and malabsorption."
    explanation: Epithelial cells express interferon-induced signatures
      associated with apoptosis and increased cell turnover, demonstrating the
      mechanism of barrier dysfunction in inflammatory colitis.
  - reference: PMID:38724705
    reference_title: "Single-cell transcriptomic analyses reveal distinct immune cell contributions to epithelial barrier dysfunction in checkpoint inhibitor colitis."
    supports: PARTIAL
    snippet: "Together, these data suggest roles for circulating T cells and epithelial-immune
      crosstalk critical to PD-1/CTLA-4-dependent tolerance and barrier function and
      identify potential therapeutic targets for irColitis."
    explanation: Epithelial-immune crosstalk is critical to barrier function,
      confirming that disruption of this interaction underlies epithelial
      barrier dysfunction in colitis.
  - reference: PMID:39438660
    reference_title: "A longitudinal single-cell atlas of anti-tumour necrosis factor treatment in inflammatory bowel disease."
    supports: PARTIAL
    snippet: "Pretreatment differences in epithelial and myeloid compartments were
      associated with remission outcomes in both diseases."
    explanation: Epithelial compartment differences predict treatment outcomes,
      emphasizing the central role of epithelial dysfunction in UC pathogenesis.
- name: Loss of Microbial Diversity
  description: >
    Reduced alpha diversity (species richness and evenness) in the colonic
    microbiome. Shannon and Chao1 indices are decreased compared to healthy
    controls, representing ecological collapse of the microbial community.
  biological_processes:
  - preferred_term: Microbiome Community Dynamics
    term:
      id: GO:0044003
      label: symbiont-mediated perturbation of host process
  downstream:
  - target: Loss of Keystone SCFA Producers
    description: Diversity loss disproportionately affects beneficial fermenters
  - target: Increased Microbial Community Instability
    description: Anna Karenina effect - dysbiotic communities become stochastic
  evidence:
  - reference: PMID:25307765
    reference_title: "Meta-analyses of human gut microbes associated with obesity and IBD."
    supports: PARTIAL
    snippet: "IBD has a consistent signature across studies and allows high classification
      accuracy of IBD from non-IBD subjects."
    explanation: Meta-analysis confirms IBD has consistent microbiota signatures
      distinguishing patients from healthy controls.

- name: Loss of Keystone SCFA Producers
  description: >
    Depletion of butyrate-producing Firmicutes, particularly Faecalibacterium
    prausnitzii, Roseburia spp., and Eubacterium rectale. These keystone taxa
    are network hubs supporting community structure through cross-feeding.
  notes: >
    F. prausnitzii is anti-inflammatory; its supernatant reduces colitis in
    animal models. Roseburia and Eubacterium are primary butyrate producers
    via the acetyl-CoA pathway.
  downstream:
  - target: Decreased Butyrate Production
    description: Loss of primary butyrate-synthesizing taxa
  evidence:
  - reference: PMID:18936492
    reference_title: "Faecalibacterium prausnitzii is an anti-inflammatory commensal bacterium identified by gut microbiota analysis of Crohn disease patients."
    supports: PARTIAL
    snippet: "A decrease in the abundance and biodiversity of intestinal bacteria
      within the dominant phylum Firmicutes has been observed repeatedly in Crohn
      disease (CD) patients."
    explanation: Sokol et al. demonstrated F. prausnitzii depletion is
      consistently observed in IBD.
  - reference: PMID:18936492
    reference_title: "Faecalibacterium prausnitzii is an anti-inflammatory commensal bacterium identified by gut microbiota analysis of Crohn disease patients."
    supports: PARTIAL
    snippet: "F. prausnitzii exhibits anti-inflammatory effects on cellular and TNBS
      colitis models, partly due to secreted metabolites able to block NF-kappaB activation
      and IL-8 production."
    explanation: F. prausnitzii has direct anti-inflammatory properties beyond
      its role as butyrate producer.

- name: Pathobiont Expansion
  description: >
    Bloom of opportunistic pathobionts including adherent-invasive E. coli (AIEC),
    Fusobacterium nucleatum, and Enterobacteriaceae. These taxa exploit the
    ecological niche vacated by depleted commensals and promote inflammation
    through LPS and direct epithelial invasion.
  downstream:
  - target: Mucosal Inflammation
    description: Pathobionts produce LPS and other pro-inflammatory molecules
  - target: Epithelial Barrier Dysfunction
    description: AIEC can invade epithelial cells and disrupt tight junctions
  evidence:
  - reference: PMID:26185088
    reference_title: "The Roles of Inflammation, Nutrient Availability and the Commensal Microbiota in Enteric Pathogen Infection."
    supports: PARTIAL
    snippet: "This is often characterized by an increased relative abundance of facultative
      anaerobic bacteria (e.g., Enterobacteriaeceae, Bacilli) and, at the same time,
      depletion of obligate anaerobic bacteria of the classes Bacteroidia and Clostridia."
    explanation: Dysbiosis in IBD involves expansion of Enterobacteriaceae
      pathobionts alongside depletion of beneficial obligate anaerobes.

- name: Decreased Butyrate Production
  description: >
    Reduced fecal short-chain fatty acid (SCFA) concentrations, particularly
    butyrate. Butyrate is the primary energy source for colonocytes (providing
    ~70% of energy needs) and exerts anti-inflammatory effects via HDAC
    inhibition and GPR109A signaling.
  biological_processes:
  - preferred_term: Short-chain Fatty Acid Metabolism
    term:
      id: GO:0046459
      label: short-chain fatty acid metabolic process
  downstream:
  - target: Impaired Colonocyte Energy Metabolism
    description: Butyrate deprivation causes epithelial energy deficit
  evidence:
  - reference: PMID:23023125
    reference_title: "A metagenome-wide association study of gut microbiota in type 2 diabetes."
    supports: NO_EVIDENCE
    snippet: "Patients with type 2 diabetes were characterized by a moderate degree
      of gut microbial dysbiosis, a decrease in the abundance of some universal butyrate-producing
      bacteria and an increase in various opportunistic pathogens."
    explanation: While this study focused on T2D, it demonstrates the general
      principle that dysbiosis involves loss of butyrate producers - a pattern
      also seen in IBD.

- name: Impaired Colonocyte Energy Metabolism
  description: >
    Colonocytes deprived of butyrate shift from beta-oxidation to glycolysis,
    causing energy deficit. This impairs tight junction maintenance, mucus
    production by goblet cells, and epithelial renewal from crypt stem cells.
  cell_types:
  - preferred_term: Colonic Epithelial Cell
    term:
      id: CL:0011108
      label: colon epithelial cell
  downstream:
  - target: Epithelial Barrier Dysfunction
    description: Energy-deprived colonocytes cannot maintain barrier integrity

- name: Increased Microbial Community Instability
  description: >
    Anna Karenina effect - dysbiotic microbiomes show increased inter-individual
    variability and temporal instability compared to healthy controls. The
    community loses resilience and may occupy an alternative stable state that
    resists therapeutic intervention.
  notes: >
    "All healthy microbiomes are alike; each dysbiotic microbiome is dysbiotic
    in its own way." This increased stochasticity complicates biomarker discovery
    and explains heterogeneous treatment responses.
  downstream:
  - target: Loss of Microbial Diversity
    description: Feedback loop - community instability promotes further
      diversity loss
  evidence:
  - reference: PMID:28836573
    reference_title: "Stress and stability: applying the Anna Karenina principle to animal microbiomes."
    supports: PARTIAL
    snippet: "The result is an 'Anna Karenina principle' for animal microbiomes, in
      which dysbiotic individuals vary more in microbial community composition than
      healthy individuals-paralleling Leo Tolstoy's dictum that 'all happy families
      look alike; each unhappy family is unhappy in its own way'."
    explanation: Zaneveld et al. demonstrated the Anna Karenina principle
      applies to disease-associated microbiomes.
- name: NLRP3 Inflammasome-Mediated Pyroptosis
  description: >
    Epithelial cell pyroptosis driven by NLRP3 inflammasome activation
    contributes to barrier disruption and inflammation. SLC6A14 promotes
    pyroptosis by upregulating NLRP3.
  cell_types:
  - preferred_term: Colonic Epithelial Cell
    term:
      id: CL:0011108
      label: colon epithelial cell
  biological_processes:
  - preferred_term: Pyroptosis
    term:
      id: GO:0070269
      label: pyroptotic inflammatory response
  evidence:
  - reference: PMID:38314135
    reference_title: "SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis."
    supports: SUPPORT
    snippet: "SLC6A14 was increased and correlated with NLRP3 in UC tissues."
    explanation: SLC6A14 expression is elevated and correlates with NLRP3 in UC
      tissues, establishing a molecular link between this transporter and
      inflammasome activation.
  - reference: PMID:38314135
    reference_title: "SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis."
    supports: SUPPORT
    snippet: "Reducing SLC6A14 decreased pyroptosis-associated proteins (ASC, IL-1β,
      IL-18, NLRP3)."
    explanation: Experimental reduction of SLC6A14 decreases
      pyroptosis-associated proteins including NLRP3, IL-1β, and IL-18,
      demonstrating the causal role of this pathway in UC.
  - reference: PMID:38314135
    reference_title: "SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3 inflammasome-mediated pyroptosis."
    supports: SUPPORT
    snippet: "SLC6A14 promotes UC pyroptosis by regulating NLRP3, suggesting the therapeutic
      potential of modulating the SLC6A14/NLRP3 axis."
    explanation: SLC6A14 promotes UC progression through NLRP3-mediated
      pyroptosis, identifying this as a key pathophysiological mechanism and
      potential therapeutic target.
phenotypes:
- name: Bloody Diarrhea
  category: Gastrointestinal
  frequency: VERY_FREQUENT
  diagnostic: true
  phenotype_term:
    preferred_term: Bloody Diarrhea
    term:
      id: HP:0025085
      label: Bloody diarrhea
  evidence:
  - reference: PMID:38724705
    reference_title: "Single-cell transcriptomic analyses reveal distinct immune cell contributions to epithelial barrier dysfunction in checkpoint inhibitor colitis."
    supports: PARTIAL
    snippet: "Luminal epithelial cells in patients with irColitis expressed PCSK9,
      PD-L1 and interferon-induced signatures associated with apoptosis, increased
      cell turnover and malabsorption."
    explanation: Epithelial apoptosis and increased cell turnover in
      inflammatory colitis leads to mucosal ulceration and bleeding, which
      manifests as bloody diarrhea.
- name: Abdominal Pain
  category: Gastrointestinal
  frequency: VERY_FREQUENT
  phenotype_term:
    preferred_term: Abdominal Pain
    term:
      id: HP:0002027
      label: Abdominal pain
  evidence:
  - reference: PMID:31272578
    reference_title: "Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "Typical symptoms on presentation are bloody diarrhea, abdominal pain, fecal urgency, and tenesmus."
    explanation: Mayo Clinic Proceedings review confirms abdominal pain as a typical presenting symptom in UC.
- name: Urgency
  category: Gastrointestinal
  frequency: VERY_FREQUENT
  notes: Fecal urgency
  phenotype_term:
    preferred_term: Fecal Urgency
    term:
      id: HP:0012701
      label: Bowel urgency
  evidence:
  - reference: PMID:30837080
    reference_title: "A comprehensive review and update on ulcerative colitis()."
    supports: SUPPORT
    snippet: "The classic presentation of UC include bloody diarrhea with or without mucus, rectal urgency, tenesmus, and variable degrees of abdominal pain that is often relieved by defecation."
    explanation: Rectal urgency is described as a classic presenting symptom of ulcerative colitis.
- name: Tenesmus
  category: Gastrointestinal
  frequency: FREQUENT
  phenotype_term:
    preferred_term: Tenesmus
    term:
      id: HP:0012702
      label: Tenesmus
  evidence:
  - reference: PMID:30837080
    reference_title: "A comprehensive review and update on ulcerative colitis()."
    supports: SUPPORT
    snippet: "The classic presentation of UC include bloody diarrhea with or without mucus, rectal urgency, tenesmus, and variable degrees of abdominal pain that is often relieved by defecation."
    explanation: Tenesmus is described as a classic presenting symptom of ulcerative colitis.
- name: Weight Loss
  category: Systemic
  frequency: FREQUENT
  phenotype_term:
    preferred_term: Weight Loss
    term:
      id: HP:0001824
      label: Weight loss
  evidence:
  - reference: PMID:25506359
    reference_title: "Determinants of Weight Loss prior to Diagnosis in Inflammatory Bowel Disease: A Retrospective Observational Study."
    supports: SUPPORT
    snippet: "51% of subjects with UC experienced significant weight loss prior to diagnosis (>5% BMI loss)."
    explanation: Weight loss is a significant and common symptom in ulcerative colitis patients, with over half experiencing significant weight loss prior to diagnosis.
- name: Fatigue
  category: Systemic
  frequency: FREQUENT
  phenotype_term:
    preferred_term: Fatigue
    term:
      id: HP:0012378
      label: Fatigue
  evidence:
  - reference: PMID:27310658
    reference_title: "Conventional treatment regimens for ulcerative colitis alleviate fatigue - an observational cohort study."
    supports: SUPPORT
    snippet: "more severe fatigue was associated with more ulcerative colitis symptoms"
    explanation: Fatigue is a common symptom in ulcerative colitis patients that correlates with disease activity and symptom severity.
- name: Anemia
  category: Hematologic
  frequency: FREQUENT
  notes: Iron deficiency from blood loss
  phenotype_term:
    preferred_term: Anemia
    term:
      id: HP:0001903
      label: Anemia
  evidence:
  - reference: PMID:25646159
    reference_title: "Anemia in inflammatory bowel disease: an under-estimated problem?"
    supports: SUPPORT
    snippet: "Anemia is one of the most frequent complications and/or extraintestinal manifestations of inflammatory bowel disease (IBD). Iron deficiency is the most important cause of anemia in Crohn's disease and ulcerative colitis patients."
    explanation: Anemia, particularly iron deficiency anemia, is one of the most frequent complications of ulcerative colitis due to chronic blood loss from the inflamed colonic mucosa.
biochemical:
- name: Fecal Calprotectin
  presence: Elevated
  context: Marker of intestinal inflammation
- name: CRP
  presence: Elevated
  context: Systemic inflammation marker
- name: ESR
  presence: Elevated
  context: Active disease
genetic:
- name: IL23R
  association: Risk Factor
- name: HNF4A
  association: Risk Factor
- name: CDH1
  association: Risk Factor
- name: HLA-DRB1
  association: Risk Factor
- name: BACH2
  association: GWAS
  notes: Transcription factor regulating Treg/effector T cell balance and B cell
    class switching
- name: TNFAIP3
  association: GWAS
  notes: Encodes A20, a ubiquitin-editing enzyme that negatively regulates NF-kB
    signaling
- name: STAT3
  association: GWAS
  notes: Signal transducer mediating Th17 differentiation via JAK-STAT pathway
- name: IL10
  association: GWAS
  notes: Anti-inflammatory cytokine critical for immune tolerance
- name: CD28
  association: GWAS
  notes: T cell co-stimulatory receptor required for T cell activation
- name: EGR2
  association: GWAS
  notes: Transcription factor involved in T cell anergy and peripheral tolerance
- name: ETS1
  association: GWAS
  notes: Transcription factor regulating T and B cell development and immune
    cell differentiation
- name: IRF8
  association: GWAS
  notes: Interferon regulatory factor controlling myeloid cell development and
    type I interferon response
- name: SATB1
  association: GWAS
  notes: Chromatin organizer regulating T cell development and lineage
    commitment
- name: IKZF1
  association: GWAS
  notes: Ikaros transcription factor essential for lymphocyte development and
    differentiation
- name: SMAD3
  association: GWAS
  notes: TGF-beta signaling mediator regulating T cell differentiation and
    immune tolerance
- name: REL
  association: GWAS
  notes: NF-kB subunit c-Rel controlling lymphocyte activation and survival
- name: PRDM1
  association: GWAS
  notes: Blimp-1 transcription factor regulating T cell and B cell terminal
    differentiation
- name: PTPN22
  association: GWAS
  notes: Protein tyrosine phosphatase modulating T cell receptor signaling
    threshold
environmental:
- name: Appendectomy
  notes: Protective effect
- name: Smoking
  notes: Protective (unlike Crohn's)
- name: NSAIDs
  notes: May trigger flares
- name: Infections
  notes: May trigger onset
- name: Stress
  notes: May trigger flares
treatments:
- name: 5-Aminosalicylates
  description: First-line for mild-moderate disease (mesalamine).
  treatment_term:
    preferred_term: 5-aminosalicylate therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:21407188
    reference_title: "Efficacy of 5-aminosalicylates in ulcerative colitis: systematic review and meta-analysis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "5-ASAs are highly effective for inducing remission and preventing relapse in UC. Evidence suggests that doses of ≥ 2.0 g/day have greater efficacy"
    explanation: Systematic review and meta-analysis confirming 5-ASA efficacy in UC remission induction and relapse prevention.
- name: Corticosteroids
  description: For acute flares (prednisone, budesonide).
  treatment_term:
    preferred_term: Corticosteroid therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:31272578
    reference_title: "Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "Most cases are treated with pharmacological therapy to first induce remission and then to maintain a corticosteroid-free remission."
    explanation: Review confirms corticosteroids are used to induce remission with goal of achieving corticosteroid-free maintenance.
- name: Thiopurines
  description: Azathioprine, 6-MP for maintenance.
  treatment_term:
    preferred_term: Thiopurine therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:31272578
    reference_title: "Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "In moderate to severe colitis, medication classes include thiopurines, biological agents targeting tumor necrosis factor and integrins, and the small-molecule Janus kinase inhibitors."
    explanation: Review confirms thiopurines as a treatment class for moderate-severe UC.
- name: Anti-TNF Therapy
  description: Infliximab, adalimumab for moderate-severe disease.
  treatment_term:
    preferred_term: Anti-TNF therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:26902011
    reference_title: "Anti-TNF-A Therapy about Infliximab and Adalimamab for the Effectiveness in Ulcerative Colitis Compared with Conventional Therapy: A Meta-Analysis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "Infliximab had a statistically significant effects in induction of clinical response (RR = 1.67; 95% CI 1.12 to 2.50) of UC compared with conventional therapy"
    explanation: Meta-analysis demonstrating significant efficacy of anti-TNF agents in UC clinical response induction.
- name: Vedolizumab
  description: Gut-selective integrin inhibitor.
  treatment_term:
    preferred_term: Vedolizumab therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:31470005
    reference_title: "Efficacy and Safety of Vedolizumab Subcutaneous Formulation in a Randomized Trial of Patients With Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "clinical remission at week 52 was achieved by 46.2%, 42.6%, and 14.3% of patients in the subcutaneous vedolizumab, intravenous vedolizumab, and placebo groups, respectively"
    explanation: Phase 3 RCT demonstrating vedolizumab efficacy with 46% clinical remission vs 14% placebo at week 52.
- name: Tofacitinib
  description: JAK inhibitor for moderate-severe disease.
  treatment_term:
    preferred_term: JAK inhibitor therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:31272578
    reference_title: "Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "In moderate to severe colitis, medication classes include thiopurines, biological agents targeting tumor necrosis factor and integrins, and the small-molecule Janus kinase inhibitors."
    explanation: Review confirms JAK inhibitors as approved treatment for moderate-severe UC.
- name: Ustekinumab
  description: IL-12/23 inhibitor.
  treatment_term:
    preferred_term: IL-12/23 inhibitor therapy
    term:
      id: MAXO:0000058
      label: pharmacotherapy
  evidence:
  - reference: PMID:39461795
    reference_title: "IL-23 inhibition for chronic inflammatory disease."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "Addressing an upstream pathological mechanism shared between these disorders, this drug class has high efficacy rates and a durable response"
    explanation: IL-23 inhibitors demonstrate high efficacy in UC by targeting upstream pathological mechanisms.
- name: Colectomy
  description: Curative surgery for refractory or complicated disease.
  treatment_term:
    preferred_term: Colectomy
    term:
      id: MAXO:0000004
      label: surgical procedure
  evidence:
  - reference: PMID:31272578
    reference_title: "Ulcerative Colitis."
    supports: SUPPORT
    evidence_source: HUMAN_CLINICAL
    snippet: "in up to 15% of cases, patients in whom medical therapy fails or who have development of dysplasia secondary to their long-standing colitis will require surgical treatment."
    explanation: Review confirms 15% of UC patients require colectomy for refractory disease or dysplasia.
experimental_models:
- name: Biopsy-derived UC colonoid air-liquid interface model
  description: >
    Biopsy-derived sigmoid colonoids differentiated as air-liquid interface
    monolayers to model epithelial architecture, mucus production, and
    pathobiont susceptibility in ulcerative colitis.
  experimental_model_type: PRIMARY_CELL_CULTURE
  namo_type: namo:TwoDCellCulture
  organism:
    preferred_term: human
    term:
      id: NCBITaxon:9606
      label: Homo sapiens
  tissue_term:
    preferred_term: colon
    term:
      id: UBERON:0001155
      label: colon
  cell_types:
  - preferred_term: Colonic Epithelial Cell
    term:
      id: CL:0011108
      label: colon epithelial cell
  conditions:
  - ulcerative colitis
  - non-IBD control
  - pathobiont challenge
  cell_source: Patient biopsy-derived sigmoid colonic epithelial crypts expanded
    as colonoids
  culture_system: Air-liquid interface colonoid monolayers with mucus and
    pathobiont challenge assays
  publication: PMID:41589595
  findings:
  - statement: UC biopsy-derived ALI colonoid monolayers retain persistent epithelial and mucus-barrier defects outside the inflamed tissue environment
    evidence:
    - reference: PMID:41589595
      reference_title: "Biopsy-derived colonoid air-liquid interface monolayers reveal persistent mucosal defects in ulcerative colitis patients."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "ALI monolayers from UC patients displayed a range of impairments, with classification ranging from a mild phenotype with distorted architecture and a thinner, more permeable mucus layer to a severe phenotype with defects in cellular differentiation and an inability to produce a mucus layer."
      explanation: Supports persistent epithelial barrier and mucus-layer defects relevant to Epithelial Barrier Dysfunction.
    - reference: PMID:34418586
      reference_title: "Chronic Inflammation in Ulcerative Colitis Causes Long-Term Changes in Goblet Cell Function."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "Differentiated UC colonoid monolayers form a thin and non-continuous mucus layer."
      explanation: Independently supports durable mucus-barrier defects in patient-derived UC colonoid monolayers.
  - statement: UC colonoid monolayers provide a tractable epithelial system for linking mucus defects to pathobiont susceptibility
    evidence:
    - reference: PMID:41589595
      reference_title: "Biopsy-derived colonoid air-liquid interface monolayers reveal persistent mucosal defects in ulcerative colitis patients."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "With the use of transcriptome analysis, we identified activated pathways associated with extracellular matrix formation and cell signaling, including numerous cancer-associated genes in UC ALI monolayers, which also proved significantly more susceptible to E. coli p19A."
      explanation: Links epithelial remodeling and barrier compromise to increased susceptibility to bacterial challenge, consistent with mucosal inflammation and host-microbe dysfunction.
    - reference: PMID:34418586
      reference_title: "Chronic Inflammation in Ulcerative Colitis Causes Long-Term Changes in Goblet Cell Function."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "Chronic inflammation in UC causes long-term changes in GCs, leading to abnormal mucus secretion."
      explanation: Supports a mechanistic connection between chronic inflammation and lasting goblet-cell secretory dysfunction in the model.
  evidence:
  - reference: PMID:41589595
    reference_title: "Biopsy-derived colonoid air-liquid interface monolayers reveal persistent mucosal defects in ulcerative colitis patients."
    supports: SUPPORT
    evidence_source: IN_VITRO
    snippet: "ALI monolayers from UC patients displayed a range of impairments, with classification ranging from a mild phenotype with distorted architecture and a thinner, more permeable mucus layer to a severe phenotype with defects in cellular differentiation and an inability to produce a mucus layer."
    explanation: Supports this as a patient-derived UC epithelial model with direct relevance to mucosal inflammation and barrier dysfunction.
- name: Cytokine-conditioned hiPSC-derived colon organoid UC model
  description: >
    Human induced pluripotent stem cell-derived colon organoids exposed to
    TNF-α, IFN-γ, and IL-1β to model UC-like epithelial injury and stromal
    inflammatory signaling.
  experimental_model_type: IPSC_DERIVED_MODEL
  namo_type: namo:Organoid
  organism:
    preferred_term: human
    term:
      id: NCBITaxon:9606
      label: Homo sapiens
  tissue_term:
    preferred_term: colon
    term:
      id: UBERON:0001155
      label: colon
  conditions:
  - ulcerative colitis-like cytokine exposure
  - TNF-α/IFN-γ/IL-1β stimulation
  - tofacitinib response testing
  cell_source: Human induced pluripotent stem cell-derived colon organoids
  culture_system: Three-dimensional colon organoid culture with pro-inflammatory
    cytokine conditioning
  publication: PMID:39435148
  findings:
  - statement: Cytokine-conditioned hiPSC colon organoids reproduce epithelial injury and inflammatory stromal responses that resemble UC tissue
    evidence:
    - reference: PMID:39435148
      reference_title: "Establishment of an ulcerative colitis model using colon organoids derived from human induced pluripotent stem cells."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "Inflammatory responses in stromal cells and damage to intestinal epithelial cells were observed in the 3CK-treated hiPSC-COs."
      explanation: Supports alignment with Dysregulated Immune Response and Epithelial Barrier Dysfunction in a human stem-cell-derived system.
    - reference: PMID:39435148
      reference_title: "Establishment of an ulcerative colitis model using colon organoids derived from human induced pluripotent stem cells."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "Comparison of molecular signatures of 3CK-treated hiPSC-COs with those of ulcerative colitis (UC) patient's colon revealed that 3CK-treated hiPSC-COs resemble UC patient's colon."
      explanation: Supports molecular resemblance of the model to UC tissue rather than generic cytokine injury alone.
  - statement: The model can be used to test whether cytokine-driven inflammatory outputs are pharmacologically reversible
    evidence:
    - reference: PMID:39435148
      reference_title: "Establishment of an ulcerative colitis model using colon organoids derived from human induced pluripotent stem cells."
      supports: SUPPORT
      evidence_source: IN_VITRO
      snippet: "Furthermore, the elevated production of inflammatory cytokines observed in 3CK-treated hiPSC-COs was attenuated by treatment with tofacitinib."
      explanation: Supports translational use of the model for pathway-focused drug testing in a UC-like inflammatory state.
  evidence:
  - reference: PMID:39435148
    reference_title: "Establishment of an ulcerative colitis model using colon organoids derived from human induced pluripotent stem cells."
    supports: SUPPORT
    evidence_source: IN_VITRO
    snippet: "Comparison of molecular signatures of 3CK-treated hiPSC-COs with those of ulcerative colitis (UC) patient's colon revealed that 3CK-treated hiPSC-COs resemble UC patient's colon."
    explanation: Supports this as a human iPSC-derived organoid model with molecular similarity to UC tissue.
- name: Human colon-on-chip mucus barrier model
  description: >
    Microfluidic human colon chip lined by primary patient-derived colonic
    epithelial cells to model mucus bilayer formation and inflammatory control
    of mucus hydration.
  experimental_model_type: ORGAN_ON_CHIP
  namo_type: namo:OrganOnChip
  organism:
    preferred_term: human
    term:
      id: NCBITaxon:9606
      label: Homo sapiens
  tissue_term:
    preferred_term: colon
    term:
      id: UBERON:0001155
      label: colon
  cell_types:
  - preferred_term: Colonic Epithelial Cell
    term:
      id: CL:0011108
      label: colon epithelial cell
  conditions:
  - mucus barrier physiology
  - prostaglandin E2 stimulation
  - ulcerative colitis-relevant mucus barrier dysfunction
  cell_source: Primary patient-derived colonic epithelial cells
  culture_system: Microfluidic colon-on-chip device with live imaging of mucus
    layer formation
  publication: PMID:31778828
  findings:
  - statement: The colon chip reproduces human colonic mucus bilayer structure, making it useful for mechanistic study of mucus-barrier defects relevant to UC
    evidence:
    - reference: PMID:31778828
      reference_title: "Human Colon-on-a-Chip Enables Continuous In Vitro Analysis of Colon Mucus Layer Accumulation and Physiology."
      supports: PARTIAL
      evidence_source: IN_VITRO
      snippet: "The Colon Chip supports spontaneous goblet cell differentiation and accumulation of a mucus bilayer with impenetrable and penetrable layers, and a thickness similar to that observed in the human colon, while maintaining a subpopulation of proliferative epithelial cells."
      explanation: Supports physiologic mucus-barrier fidelity in a human colon microphysiological system relevant to UC barrier biology.
    - reference: PMID:31778828
      reference_title: "Human Colon-on-a-Chip Enables Continuous In Vitro Analysis of Colon Mucus Layer Accumulation and Physiology."
      supports: PARTIAL
      evidence_source: IN_VITRO
      snippet: "The Colon Chip may offer a new preclinical tool to analyze the role of mucus in human intestinal homeostasis as well as diseases, such as ulcerative colitis and cancer."
      explanation: Supports inclusion as a restrained UC-adjacent organ-on-chip bridge rather than a direct disease-specific UC model.
  - statement: The chip captures inflammatory mediator effects on mucus hydration without requiring animal models
    evidence:
    - reference: PMID:31778828
      reference_title: "Human Colon-on-a-Chip Enables Continuous In Vitro Analysis of Colon Mucus Layer Accumulation and Physiology."
      supports: PARTIAL
      evidence_source: IN_VITRO
      snippet: "Live imaging of the mucus layer formation on-chip showed that stimulation of the colonic epithelium with prostaglandin E2, which is increased during inflammation, causes rapid mucus volume expansion via an Na-K-Cl cotransporter 1 ion channel-dependent increase in its hydration state, but no increase in de novo mucus secretion."
      explanation: Connects the platform to inflammatory mediator responses relevant to mucosal inflammation and mucus-layer physiology in UC.
  evidence:
  - reference: PMID:31778828
    reference_title: "Human Colon-on-a-Chip Enables Continuous In Vitro Analysis of Colon Mucus Layer Accumulation and Physiology."
    supports: PARTIAL
    evidence_source: IN_VITRO
    snippet: "A human colon-on-a-chip (Colon Chip) microfluidic device lined by primary patient-derived colonic epithelial cells was used to recapitulate mucus bilayer formation, and to visualize mucus accumulation in living cultures noninvasively."
    explanation: Supports this as a human colon organ-on-chip platform for studying mucus-barrier mechanisms relevant to UC.
computational_models:
- name: AGORA2 Gut Microbiome Metabolic Models
  description: >
    Collection of 7,302 strain-resolved genome-scale metabolic reconstructions of
    human
    gut microorganisms. Enables modeling of UC-associated dysbiosis including loss
    of
    keystone SCFA producers (F. prausnitzii, Roseburia, Eubacterium rectale) and expansion
    of pathobionts (Fusobacterium, Enterobacteriaceae). Supports colonocyte energy
    metabolism
    modeling.
  model_type: GENOME_SCALE_METABOLIC
  repository_url: https://www.vmh.life/
  publication: PMID:36543475
  notes: Nature Biotechnology 2022 - strain-level resolution for butyrate
    producer depletion studies
- name: MICOM Community Metabolic Model
  description: >
    Metagenome-scale modeling framework for simulating metabolic interactions in the
    gut microbiota. Models decreased butyrate production, impaired colonocyte energy
    metabolism, and Anna Karenina effect (increased community instability) observed
    in
    UC. Integrates with dietary intervention modeling.
  model_type: GENOME_SCALE_METABOLIC
  model_software: COBRApy
  publication: PMID:31964767
  notes: mSystems 2020 - enables personalized SCFA flux predictions from patient
    metagenomes
- name: Host-Microbiome Multi-Objective Optimization Model
  description: >
    Integrated metabolic model combining human colonic epithelial cell metabolism
    with
    gut microbiome community models. Predicts metabolic crosstalk disruption in UC,
    including butyrate deprivation effects on colonocyte beta-oxidation and tight
    junction
    maintenance.
  model_type: GENOME_SCALE_METABOLIC
  publication: PMID:38729159
  notes: iScience 2024 - models host-microbiome metabolic interactions at
    community scale
datasets:
# CELLxGENE - IBD single-cell atlas
- accession: "cellxgene:7c7bd6c2-925b-4034-baab-620ef1b760e1"
  title: Human inflammatory bowel disease (IBD) and healthy control 10x Single-cell transcriptomics data
  description: >-
    Single-cell transcriptomic atlas of human inflammatory bowel disease including
    ulcerative colitis and Crohn disease samples alongside healthy controls.
    Characterizes immune and epithelial cell populations in inflamed intestinal
    tissue.
  organism:
    preferred_term: human
    term:
      id: NCBITaxon:9606
      label: Homo sapiens
  data_type: SINGLE_CELL_RNA_SEQ
  sample_types:
  - preferred_term: colon tissue
    tissue_term:
      preferred_term: colon
      term:
        id: UBERON:0001155
        label: colon
  conditions:
  - ulcerative colitis
  - Crohn disease
  - normal
  publication: PMID:37488103
  notes: CZI CELLxGENE collection. DOI 10.1038/s41467-023-40156-6. Covers both UC and CD for comparative analysis.

references:
- reference: DOI:10.1038/s41590-024-01994-8
  title: A longitudinal single-cell atlas of anti-tumour necrosis factor
    treatment in inflammatory bowel disease
  findings: []
- reference: DOI:10.1038/s41591-024-02895-x
  title: Single-cell transcriptomic analyses reveal distinct immune cell
    contributions to epithelial barrier dysfunction in checkpoint inhibitor
    colitis
  findings: []
- reference: DOI:10.3389/fcimb.2025.1626614
  title: 'Fucoidan as a therapeutic agent for ulcerative colitis: mechanisms of action
    and modulation of the gut microbiota'
  findings: []
- reference: DOI:10.3390/biomedicines13020305
  title: Novel Insights into the Pathogenesis of Inflammatory Bowel Diseases
  findings: []
- reference: DOI:10.3748/wjg.v30.i3.252
  title: SLC6A14 promotes ulcerative colitis progression by facilitating NLRP3
    inflammasome-mediated pyroptosis
  findings: []